Juvenile Xanthogranuloma of Middle Ear and External Auditory Canal: A Rare Case Report

Saleh E^1*, Shaikh A², Jastania R¹ and Zuraiqi BA³

¹Department of ENT and Head Neck Surgery, King Abdullah Medical City, Makkah, Saudi Arabia

²Alexandria University, Faculty of Medicine, Egypt

³Department of Histopathology, King Abdullah Medical City, Makkah, Saudi Arabia

*Corresponding Author : Essam Saleh
Department of ENT and Head Neck Surgery, King Abdullah Medical City, Muzadalafa Road, Makkah 21955, P.O.BOX 57657, Kingdom of Saudi Arabia
Tel: 012 554999 ext. 17172/17174
E-mail: salehessam@yahoo.com

Received: July 15, 2016 Accepted: May 11, 2017 Published: June 18, 2017

Citation: Saleh E, Shaikh A, Jastania R, Zuraiqi BA (2017) Juvenile Xanthogranuloma of Middle Ear and External Auditory Canal: A Rare Case Report. J Otol Rhinol 6:3. doi: 10.4172/2324-8785.1000313

Juvenile xanthogranuloma (JXG) is a benign self-limiting non langerhans cell histiocytic lesion of unknown etiology and pathogenesis. It commonly affects infants and adolescents only 15% cases reported from the adult population. It characteristically appears as yellow to brown solitary papule, affecting the skin of head, neck and trunk region. Extra cutaneous JXG are reported from various sites including central nervous system, gastrointestinal system, kidney, larynx, tongue with single case report from tympanic membrane and external auditory canal. We describe a very rare case of adult JXG occurring as multiple papules from the external auditory canal and granulations from middle ear, which presented as persistent otorrhea. We discuss the clinical presentation, imaging, pathological findings and review of literature for this case. To the best of our knowledge this is first reported case of JXG from the middle ear cavity.