Sporadic Lymphangioleiomyomatosis Presented with Bilateral Pneumothorax

A 41-year old lady in a reproductive age group presented to us with bilateral pneumothorax. She gave history of right sided pneumothorax prior to this episode which prompted us to further investigate which revealed multiple bilateral cystic lung changes on high resolution computed tomography of the thorax. Transbronchial cryobiopsy of the lung confirmed the diagnosis of lymphangioleiomyomatosis. She was treated conservatively due to financial constraints and discharged two months later once prolonged air leak resolved. This case illustrates the need to investigate the underlying cause of recurrent pneumothorax especially in females due to therapeutic and prognostic implications.